Segmental neurofibromatosis (NF-5): a rare form of neurofibromatosis.

Neurofibromatosis is a common disorder that affects approximately 1 in 3000 persons [1]. Segmental neurofibromatosis is a rare form of the disease in which the cutaneous and neural changes are confined to one region of the body. Because the natural history and genetics of the segmental type may be different from those of the more common forms, it is important to become familiar with this unusual disorder.